|
Hormonal profile and GnRH stimulation test in adult female patients with KS. |
||||||||||
| FAMILY |
Age |
Inheritance |
Base line LH (mIU/ml) N= |
Peak LH (mIU/ml) after GnRH testing |
Peak LH (mIU/ml) after priming |
Base line FSH (mIU/ml) N= |
Peak FSH (mIU/ml) After GnRH testing |
Peak FSH (mIU/ml) after priming |
Estradiol Pg/ml |
|
|
|
||||||||||
| X |
1 |
23 |
AR |
0.6 |
7.25 |
2.6 |
19.33 |
5 |
||
| 2 |
21 |
AR |
0.5 |
3.5 |
1.95 |
6.60 |
7 |
|||
| 3 |
18 |
AR |
0.6 |
5.2 |
1.2 |
9.5 |
10 |
|||
| IX |
1 |
18 |
sporadic |
0.8 |
5.10 |
2.1 |
5.6 |
15 |
||
| XI |
1 |
30 |
sporadic |
0.7 |
4.2 |
1.5 |
6.2 |
10 |
||
| XII |
1 |
18 |
sporadic |
Undetected |
2.10 |
2.1 |
5.8 |
Undetected |
||
|
AR :autosomal recessive | ||||||||||
AbuJbara et al. Reproductive Health 2004 1:5 doi:10.1186/1742-4755-1-5 |
||||||||||